Podcast #144: Moya Moya

9d90df71-0f05-4e59-9101-dcf2815820e4Run Time: 5 minutes

Author: Gretchen Hinson M.D.

Educational Pearls:

  • Etymology: the Japanese expression for “hazy just like a puff of cigarette smoke drifting in the air”, named because angiographic images of a brain with Moyamoya make the blood vessels look like a puff of smoke.
  • A patient with moyamoya will have bilateral stenosis of the vessels at the base of brain at the circle of Willis resulting in collateral circulation that is unstable and leads to hemorrhagic and thrombotic events.
  • Moyamoya disease is idiopathic. However, there are multiple predispositions: sickle cell, any vasculitis or vasculopathy, neurofibromatosis, genetic disorders (down’s syndrome), autoimmune disorders, and brain irradiation as a child.
  • Hallmark presentation for moyamoya are young patients presenting for stroke like symptoms who have comorbidities that predispose him/her to develop stenosis and vascular abnormalities.

Link to Podcast: http://medicalminute.madewithopinion.com/moyamoya/

References: http://www.ninds.nih.gov/disorders/moyamoya/moyamoya.htm

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